{"id":1788,"date":"2005-10-01T01:00:00","date_gmt":"2005-10-01T00:00:00","guid":{"rendered":"https:\/\/angh.net\/abstracts\/une-evolution-histologique-inhabituelle-dun-syndrome-de-chevauchement-cbp-hai-traite-par-acide-ursodesoxycholique\/"},"modified":"2018-10-20T18:39:37","modified_gmt":"2018-10-20T16:39:37","slug":"une-evolution-histologique-inhabituelle-dun-syndrome-de-chevauchement-cbp-hai-traite-par-acide-ursodesoxycholique","status":"publish","type":"post","link":"https:\/\/angh.net\/abstracts\/une-evolution-histologique-inhabituelle-dun-syndrome-de-chevauchement-cbp-hai-traite-par-acide-ursodesoxycholique\/","title":{"rendered":"UNE EVOLUTION HISTOLOGIQUE INHABITUELLE D\u2019UN SYNDROME DE CHEVAUCHEMENT CBP-HAI TRAITE PAR ACIDE URSODESOXYCHOLIQUE"},"content":{"rendered":"<p><strong>2005<\/strong><\/p>\n<p><em>C Renou (1), M Bourli\u00e8re (2), F Martini (3), O Larroque (1), B Calvet (3), S Sokolowsky (3), A Harafa (1), JP Igual (1), T Benderitter (4), P Halfon (5).Unit\u00e9 d\u2019h\u00e9pato-gastroent\u00e9rologie, CH Hy\u00e8res (1) ; Service d\u2019h\u00e9pato-gastroent\u00e9rologie, H\u00f4pital Saint-Joseph, Marseille (2) ; Laboratoire d\u2019anatomo-pathologie, Toulon (3) ; Cabinet d\u2019h\u00e9pato-gastroent\u00e9rologie, boulevard de Strasbourg, Toulon (4) ; Laboratoire de virologie, Alphabio, Marseille (5)<\/em><\/p>\n<p><strong>H\u00e9patologie <\/strong>&#8211; \u00a02005-06-02 &#8211;\u00a0PW &#8211;<\/p>\n<p>________________________________<\/p>\n<p>L\u2019absence de m\u00e9thodologie diagnostique unique dans les syndromes de chevauchement entre cirrhose biliaire primitive (CBP) et h\u00e9patite auto-immune (HAI) t\u00e9moigne de la raret\u00e9 et de l\u2019absence de validation prospective de cette pathologie auto-immune. Toutefois, la m\u00e9thodologie fran\u00e7aise (Chazouill\u00e8res et al., Hepatology 1998) bas\u00e9e sur la pr\u00e9sence de deux des trois crit\u00e8res diagnostiques reconnus pour chacune des deux pathologies, reste la plus pertinente et de fait la plus employ\u00e9e. Le traitement du syndrome de chevauchement CBP-HAI est mal codifi\u00e9. L\u2019association acide ursod\u00e9soxycholique-corticoth\u00e9rapie pourrait \u00eatre le traitement de choix du syndrome de chevauchement au travers de r\u00e9sultats encourageants de diff\u00e9rentes \u00e9tudes th\u00e9rapeutiques (Chazouill\u00e8res et al., Hepatology 1998 ; Lohse et al., Hepatology 1999). Toutefois, la prescription d\u2019acide ursod\u00e9soxycholique en monoth\u00e9rapie semblerait \u00eatre \u00e9galement efficace \u00e0 la fois sur le plan biochimique et immunologique en l\u2019absence d\u2019effet secondaire grave associ\u00e9 (Joshi et al., Hepatology 2002).<\/p>\n<p>Le diagnostic de syndrome de chevauchement CBP-HAI \u00e9tait pos\u00e9 chez un homme de 48 ans dans les suites d\u2019un bilan d\u2019asth\u00e9nie isol\u00e9e. L\u2019activit\u00e9 des ALAT \u00e9tait sup\u00e9rieure \u00e0 5N et celle des phosphatases alcalines \u00e0 2N. La recherche d\u2019anticorps anti-mitochondries de type M2 \u00e9tait positive (1\/1640i\u00e8me) en IFI et par Western blot. L\u2019examen histologique h\u00e9patique mettait en \u00e9vidence une h\u00e9patite mod\u00e9r\u00e9e de l\u2019interface et des canaux biliaires normaux. Un traitement par acide ursod\u00e9soxycholique \u00e9tait prescrit \u00e0 la dose de 15 mg\/Kg\/j. La r\u00e9gression de la cholestase et la cytolyse survenait apr\u00e8s 3 mois de traitement puis se maintenait jusqu\u2019\u00e0 la r\u00e9alisation d\u2019une nouvelle ponction biopsie h\u00e9patique effectu\u00e9e apr\u00e8s 18 mois de traitement. L\u2019examen histologique h\u00e9patique \u00e9tait normal. La poursuite du traitement \u00e9tait maintenue du fait de la m\u00e9connaissance de l\u2019histoire naturelle du syndrome de chevauchement CBP-HAI non trait\u00e9.<\/p>\n<p>A notre connaissance, il s\u2019agit du premier cas de r\u00e9gression compl\u00e8te des perturbations biochimiques et histologiques apr\u00e8s traitement d\u2019un syndrome de chevauchement CBP-HAI par acide ursod\u00e9soxycholique. Cette observation renforce l\u2019int\u00e9r\u00eat de la prescription d\u2019acide ursod\u00e9soxycholique, sans corticoth\u00e9rapie associ\u00e9e, lors de la prise en charge th\u00e9rapeutique initiale d\u2019un syndrome de chevauchement CBP-HAI.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>2005 C Renou (1), M Bourli\u00e8re (2), F Martini (3), O Larroque (1), B Calvet (3), S Sokolowsky (3), A Harafa (1), JP Igual (1), T Benderitter (4), P Halfon (5).Unit\u00e9 d\u2019h\u00e9pato-gastroent\u00e9rologie, CH Hy\u00e8res (1) ; Service d\u2019h\u00e9pato-gastroent\u00e9rologie, H\u00f4pital Saint-Joseph, Marseille (2) ; Laboratoire d\u2019anatomo-pathologie, Toulon (3) ; Cabinet d\u2019h\u00e9pato-gastroent\u00e9rologie, boulevard de Strasbourg, Toulon (4) [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[3],"tags":[16],"class_list":["post-1788","post","type-post","status-publish","format-standard","hentry","category-hepatologie","tag-16"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.2 - 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