{"id":1847,"date":"2008-10-01T01:00:00","date_gmt":"2008-10-01T00:00:00","guid":{"rendered":"https:\/\/angh.net\/abstracts\/melanome-malin-revele-par-des-metastases-jejunales-hemorragiques\/"},"modified":"2018-10-20T18:39:48","modified_gmt":"2018-10-20T16:39:48","slug":"melanome-malin-revele-par-des-metastases-jejunales-hemorragiques","status":"publish","type":"post","link":"https:\/\/angh.net\/abstracts\/melanome-malin-revele-par-des-metastases-jejunales-hemorragiques\/","title":{"rendered":"M\u00e9lanome malin r\u00e9v\u00e9l\u00e9 par des m\u00e9tastases j\u00e9junales h\u00e9morragiques."},"content":{"rendered":"<p><strong>2008<\/strong><\/p>\n<p><em>Vincent QUENTIN (1), Olivier NOUEL (1), Marc PORNEUF (2), Pierre Marie GIRARDOT (3).<br \/>\n(1) Service d&rsquo;h\u00e9patogastroent\u00e9rologie, Centre Hospitalier Y. Le Foll, Saint Brieuc<br \/>\n(2) Service d&rsquo;onco-h\u00e9matologie, Centre Hospitalier Y. Le Foll, Saint Brieuc<br \/>\n(3) Cabinet d&rsquo;anatomie et de cytologie pathologiques, Pl\u00e9rin<\/em><\/p>\n<p><strong>Endoscopie <\/strong>&#8211; \u00a02008-06-12 &#8211;\u00a0 &#8211;<\/p>\n<p>________________________________<\/p>\n<p>Un homme de 75 ans est admis au centre hospitalier pour m\u00e9l\u00e9na au mois de mars 2008. Ses ant\u00e9c\u00e9dents essentiels comportent une cardiopathie isch\u00e9mique avec infarctus en 2001 trait\u00e9 par angioplastie et stent coronarien, une art\u00e9riopathie des membres inf\u00e9rieurs avec angioplastie poplit\u00e9 gauche en 2004, des \u00e9pisodes d\u2019embolie pulmonaire en 1993, 1997 et 2004 sans cause d\u00e9clenchante au bilan \u00e9tiologique. Son traitement habituel comprend notamment du Pr\u00e9viscan\u00ae et du Kardegic\u00ae.<\/p>\n<p>L\u2019\u00e9pisode de m\u00e9l\u00e9na est associ\u00e9 \u00e0 une an\u00e9mie normocytaire \u00e0 7g\/dl, l\u2019INR est \u00e0 2,98. Le reste du bilan biologique montre un bilan martial et vitaminique normal, une haptoglobine normale et une ur\u00e9e sanguine augment\u00e9e \u00e0 10,5 mmol\/l pour une cr\u00e9atinin\u00e9mie normale \u00e0 64 \u00b5mol\/l.<br \/>\nIl est r\u00e9alis\u00e9 une oesogastroscopie qui montre une antrite \u00e9rosive et une l\u00e9sion polypo\u00efde d\u2019allure villeuse de 15 mm de diam\u00e8tre du deuxi\u00e8me duod\u00e9num. L\u2019examen histologique des biopsies r\u00e9v\u00e8le un ad\u00e9nome villeux en dysplasie de bas grade. Sur aucune de ces l\u00e9sions il n\u2019existe de stigmate d\u2019h\u00e9morragie r\u00e9cente.<br \/>\nUne il\u00e9o-coloscopie est rapidement r\u00e9alis\u00e9e et diagnostique une diverticulose sigmo\u00efdienne et du m\u00e9l\u00e9na s\u2019\u00e9tendant du colon \u00e0 l\u2019il\u00e9on terminal. Dans le m\u00eame temps anesth\u00e9sique il est refait une oesogastroduod\u00e9noscopie qui montre un saignement actif en nappe de l\u2019ad\u00e9nome villeux du D2, un traitement par clip h\u00e9mostatique est r\u00e9alis\u00e9.<br \/>\nDevant la persistance du m\u00e9l\u00e9na et la r\u00e9cidive de l\u2019an\u00e9mie un examen par vid\u00e9ocapsule de l\u2019intestin gr\u00eale est r\u00e9alis\u00e9 \u00e0 J 9 et r\u00e9v\u00e8le au moins 6 l\u00e9sions j\u00e9junales h\u00e9morragiques dont 2 semblent d\u2019allure tumorale car \u00e0 berges irr\u00e9guli\u00e8res, sur\u00e9lev\u00e9es et ulc\u00e9r\u00e9es. L\u2019il\u00e9on n\u2019est pas bien visualis\u00e9 du fait du m\u00e9l\u00e9na.<br \/>\nIl est alors pratiqu\u00e9 \u00e0 J 14 une ent\u00e9roscopie haute qui confirme l\u2019existence de 6 \u00e0 7 l\u00e9sions semblables du j\u00e9junum. Il s\u2019agit de l\u00e9sions rondes, ulc\u00e9r\u00e9es en leur centre avec des berges villeuses. Certaines de ces ulc\u00e9rations pr\u00e9sentent un caillot adh\u00e9rent. Des biopsies sont pratiqu\u00e9es.<\/p>\n<p>L\u2019examen anatomo pathologique montre une infiltration par plage tr\u00e8s dense de cellules avec noyau hypernucl\u00e9ol\u00e9 et cytoplasme fortement \u00e9osinophile. Il existe 5 mitoses\/10 champs et il est observ\u00e9 des d\u00e9p\u00f4ts pigmentaires, en motte de couleur brune. L\u2019immunoph\u00e9notypage est positif sur l\u2019anti-PS100 et l\u2019anti-m\u00e9lan-A, n\u00e9gatif sur l\u2019anti-CLA et l\u2019anti-CD117. Ces r\u00e9sultats orientent vers le diagnostic de m\u00e9tastases j\u00e9junales d\u2019un m\u00e9lanome malin.<\/p>\n<p>La recherche d\u2019une tumeur primitive est n\u00e9gative (examen dermatologique, ORL, ophtalmologique et proctologique). La tomodensitom\u00e9trie c\u00e9r\u00e9brale et thoraco abdominale ne met pas en \u00e9vidence de l\u00e9sion. En revanche un PET-Scan au 18F-FDG r\u00e9v\u00e9le qu\u2019il existe d\u2019ind\u00e9nombrable localisations secondaires pulmonaires bilat\u00e9rales, ganglionnaires sus et sous diaphragmatique, musculaires (dont intra-cardiaque), h\u00e9patiques, digestives, intra abdominale (carcinose) et osseuses.<\/p>\n<p>Un traitement palliatif par chimioth\u00e9rapie de type Detic\u00e8ne est propos\u00e9 apr\u00e8s passage en RCP sp\u00e9cialis\u00e9e. La tol\u00e9rance est marqu\u00e9e par une an\u00e9mie avec besoins transfusionnel r\u00e9guliers mais sans ext\u00e9riorisation digestive.<\/p>\n<p>Ce cas clinique de m\u00e9tastases j\u00e9junale d\u2019un m\u00e9lanome malin permet de pr\u00e9senter des images endoscopiques typiques (y compris en vid\u00e9o capsule). Il permet \u00e9galement de pr\u00e9ciser que les m\u00e9tastases de l\u2019intestin gr\u00eale d\u2019un m\u00e9lanome sont fr\u00e9quentes (&#8776;50%) mais rarement diagnostiqu\u00e9es avant le d\u00e9c\u00e8s (&lt;5%) et sont exceptionnellement le mode de r\u00e9v\u00e9lation de la maladie. Enfin ce cas rappelle l\u2019apport de la vid\u00e9ocapsule dans l\u2019exploration en urgence de l\u2019intestin gr\u00eale en cas d\u2019h\u00e9morragie digestive inexpliqu\u00e9e par les endoscopies standards.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>2008 Vincent QUENTIN (1), Olivier NOUEL (1), Marc PORNEUF (2), Pierre Marie GIRARDOT (3). (1) Service d&rsquo;h\u00e9patogastroent\u00e9rologie, Centre Hospitalier Y. Le Foll, Saint Brieuc (2) Service d&rsquo;onco-h\u00e9matologie, Centre Hospitalier Y. Le Foll, Saint Brieuc (3) Cabinet d&rsquo;anatomie et de cytologie pathologiques, Pl\u00e9rin Endoscopie &#8211; \u00a02008-06-12 &#8211;\u00a0 &#8211; ________________________________ Un homme de 75 ans est admis [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[6],"tags":[19],"class_list":["post-1847","post","type-post","status-publish","format-standard","hentry","category-endoscopie","tag-19"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.2 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>M\u00e9lanome malin r\u00e9v\u00e9l\u00e9 par des m\u00e9tastases j\u00e9junales h\u00e9morragiques. - Abstracts des congr\u00e8s de l&#039;ANGH<\/title>\n<meta name=\"description\" content=\"ANGH R\u00e9sum\u00e9s congr\u00e8s H\u00e9patologie Gastroent\u00e9romogie Hepatology Gastroenterology Etudes cliniques Clinical study\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/angh.net\/abstracts\/melanome-malin-revele-par-des-metastases-jejunales-hemorragiques\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"M\u00e9lanome malin r\u00e9v\u00e9l\u00e9 par des m\u00e9tastases j\u00e9junales h\u00e9morragiques. - 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