{"id":1863,"date":"2009-10-01T01:00:00","date_gmt":"2009-10-01T00:00:00","guid":{"rendered":"https:\/\/angh.net\/abstracts\/une-sclerose-mesenterique-revelant-une-cholangite-sclerosante-primitive\/"},"modified":"2018-10-20T18:39:48","modified_gmt":"2018-10-20T16:39:48","slug":"une-sclerose-mesenterique-revelant-une-cholangite-sclerosante-primitive","status":"publish","type":"post","link":"https:\/\/angh.net\/abstracts\/une-sclerose-mesenterique-revelant-une-cholangite-sclerosante-primitive\/","title":{"rendered":"Une scl\u00e9rose m\u00e9sent\u00e9rique r\u00e9v\u00e9lant une cholangite scl\u00e9rosante primitive ?"},"content":{"rendered":"<p><strong>2009<\/strong><\/p>\n<p><em>Audrey Weber, Olivier Duhamel, St\u00e9phanie Faure, Laurent Passebois, Philippe Dambron, Yann Le Bricquir, Mohamed Ramdani. P\u00f4le Visc\u00e9ral, Centre Hospitalier, F-34525 BEZIERS<\/em><\/p>\n<p><strong>H\u00e9patologie <\/strong>&#8211; \u00a02009-06-04 &#8211;\u00a0PW &#8211;<\/p>\n<p>________________________________<\/p>\n<p>Mr A. p\u00e2tissier de 43 ans, est admis le 9 mars 2009 pour asth\u00e9nie, douleur abdominale mod\u00e9r\u00e9e et amaigrissement de 5 kg en 4 mois. Un diagnostic de maladie coeliaque avait \u00e9t\u00e9 pos\u00e9 \u00e0 l\u2019\u00e2ge de 8 ans, et le r\u00e9gime n\u00e9glig\u00e9 depuis l\u2019adolescence. Cliniquement, poids 41 kg ( poids de forme \u00e0 46 kg pour 1.65 m) et diminution du murmure v\u00e9siculaire de la base droite. Biologiquement, PAL 11N, GGT 17N, ASAT 6N, ALAT 7N, albumin\u00e9mie 26g\/l, hyperleucocytose neutrophile et thrombocytose 600 000\/mm3, CRP 34mg\/l , anticorps anti-transglutaminases et anti-endomysium absents ; les examens immunologiques et s\u00e9rologiques sont sans particularit\u00e9. En gastroscopie la muqueuse est d\u00e9polie et l\u2019histologie en faveur d\u2019une atrophie villositaire subtotale avec lymphocytose intra\u00e9pith\u00e9liale significative. A l\u2019\u00e9chographie, h\u00e9patom\u00e9galie homog\u00e8ne avec ad\u00e9nopathies c\u0153liaques et hilaires centim\u00e9triques. La tomodensitom\u00e9trie (TDM) confirme l\u2019\u00e9panchement pleural droit avec aspect infiltr\u00e9 du hile h\u00e9patique et de la r\u00e9gion coeliaque, et distension mod\u00e9r\u00e9e et diffuse des anses gr\u00eales. Un r\u00e9gime sans gluten est suivi scrupuleusement pendant un mois en centre sp\u00e9cialis\u00e9. Cependant, l\u2019\u00e9tat g\u00e9n\u00e9ral se d\u00e9grade et Mr A.. devient ict\u00e9rique (PAL 20N, GGT 50N, BT 10N, BC 15N). Afin d\u2019\u00e9liminer le diagnostic de lymphome T, plusieurs examens sont r\u00e9alis\u00e9s (PBF, Echo-endoscopie bilio-pancr\u00e9atique, gastroscopie, cholangioIRM, et TDM) mais aucun ne permet d\u2019affirmer le diagnostic. Une laparotomie exploratrice montre un gr\u00eale fragile sans l\u00e9sion intraluminale, la racine du m\u00e9sent\u00e8re et le hile h\u00e9patique sont infiltr\u00e9s et inflammatoires avec des nodules centim\u00e9triques dont l\u2019ex\u00e9r\u00e8se laisse sourdre un liquide crayeux. L\u2019histologie montre un tissu conjonctif fibreux contenant des \u00e9l\u00e9ments lympho\u00efdes avec des centres germinatifs au sein d\u2019un tissu adipeux. A ce stade, le diagnostic de scl\u00e9rose m\u00e9sent\u00e9rique est \u00e9voqu\u00e9. Une thoracoscopie \u00e9limine le diagnostic de m\u00e9soth\u00e9liome. La cholangiographie perendoscopique montre des images en \u00ab arbre mort \u00bb \u00e9vocatrices de cholangite scl\u00e9rosante. Un traitement par acide ursod\u00e9xoxycholique \u00e0 la dose de 15mg\/kg\/jour associ\u00e9 \u00e0 un traitement par corticoides \u00e0 la dose de 40mg\/jour est d\u00e9but\u00e9. L\u2019\u00e9tat g\u00e9n\u00e9ral et la biologie h\u00e9patique s\u2019am\u00e9liore progressivement.<\/p>\n<p>( PS : il y a une image scanographique de l&rsquo;engainement hilaire et coeliaque que nous aimerions joindre)<\/p>\n","protected":false},"excerpt":{"rendered":"<p>2009 Audrey Weber, Olivier Duhamel, St\u00e9phanie Faure, Laurent Passebois, Philippe Dambron, Yann Le Bricquir, Mohamed Ramdani. P\u00f4le Visc\u00e9ral, Centre Hospitalier, F-34525 BEZIERS H\u00e9patologie &#8211; \u00a02009-06-04 &#8211;\u00a0PW &#8211; ________________________________ Mr A. p\u00e2tissier de 43 ans, est admis le 9 mars 2009 pour asth\u00e9nie, douleur abdominale mod\u00e9r\u00e9e et amaigrissement de 5 kg en 4 mois. Un diagnostic [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[3],"tags":[20],"class_list":["post-1863","post","type-post","status-publish","format-standard","hentry","category-hepatologie","tag-20"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.2 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Une scl\u00e9rose m\u00e9sent\u00e9rique r\u00e9v\u00e9lant une cholangite scl\u00e9rosante primitive ? - Abstracts des congr\u00e8s de l&#039;ANGH<\/title>\n<meta name=\"description\" content=\"ANGH R\u00e9sum\u00e9s congr\u00e8s H\u00e9patologie Gastroent\u00e9romogie Hepatology Gastroenterology Etudes cliniques Clinical study\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/angh.net\/abstracts\/une-sclerose-mesenterique-revelant-une-cholangite-sclerosante-primitive\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Une scl\u00e9rose m\u00e9sent\u00e9rique r\u00e9v\u00e9lant une cholangite scl\u00e9rosante primitive ? 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