{"id":1941,"date":"2012-10-01T01:00:00","date_gmt":"2012-10-01T00:00:00","guid":{"rendered":"https:\/\/angh.net\/abstracts\/sarcoidose-digestive-revelee-par-une-pancreatite-aigue\/"},"modified":"2018-10-20T18:40:01","modified_gmt":"2018-10-20T16:40:01","slug":"sarcoidose-digestive-revelee-par-une-pancreatite-aigue","status":"publish","type":"post","link":"https:\/\/angh.net\/abstracts\/sarcoidose-digestive-revelee-par-une-pancreatite-aigue\/","title":{"rendered":"SARCOIDOSE DIGESTIVE REVELEE PAR UNE PANCREATITE AIGUE"},"content":{"rendered":"<p><strong>2012<\/strong><\/p>\n<p><em>Laurence MARTIN. Jacques DENIS, Fatima DAOUDI, Leila MANSOUR, B\u00e9n\u00e9dicte LAMBARE<br \/>\nService h\u00e9pato gastro ent\u00e9rologie, Centre Hospitalier Sud Francilien, 116 Boulevard Jean Jaur\u00e8s, 91100 CORBEIL ESSONNES<\/em><\/p>\n<p><strong>Gastroent\u00e9rologie <\/strong>&#8211; \u00a02012-05-04 &#8211;\u00a0Cho &#8211;<\/p>\n<p>________________________________<\/p>\n<p>Une patiente de 29 ans d\u2019origine maghr\u00e9bine sans ant\u00e9c\u00e9dent particulier, est hospitalis\u00e9e en urgence le 18\/02\/2011 pour violentes douleurs \u00e9pigastriques \u00e0 irradiation dorsale \u00e9voluant depuis plusieurs heures, s\u2019accompagnant de vomissements. L\u2019examen clinique est normal hors un aspect de conjonctivite.<br \/>\nBiologiquement : NFS, CRP, ionogramme, ur\u00e9e, glyc\u00e9mie, calc\u00e9mie, glyc\u00e9mie, bilan lipidique, transaminases, GGT, phosphatases alcalines, \u00e9lectrophor\u00e8se des protides, TP normaux. Lipas\u00e9mie \u00e0 2 443 UI\/l (N&lt;60)<br \/>\nScanner abdominal : pancr\u00e9as l\u00e9g\u00e8rement augment\u00e9 de volumue, homog\u00e8ne, discr\u00e8te infiltration diffuse de la graisse p\u00e9ri-pancr\u00e9atique, pas de calcification (pancr\u00e9atite aigue grade C de Balthazar), pas de lithiase biliaire.<br \/>\nLa cause de cette pancr\u00e9atite aigu\u00eb reste ind\u00e9termin\u00e9e : absence d\u2019exposition toxique (alcool, m\u00e9dicaments, toxiques industriels), pas de lithiase biliaire, de contage viral, d\u2019anomalies m\u00e9taboliques ; le dosage de l\u2019IGg4 est normal. Une pancr\u00e9ato \u2013cholangio-IRM et une \u00e9cho-endoscopie bilio-pancr\u00e9atique sont r\u00e9alis\u00e9es \u00e0 distance : normales.<br \/>\nDans les six mois suivants, elle pr\u00e9sente plusieurs nouvelles crises douloureuses vesp\u00e9rales, sans anomalies biologiques. Une nouvelle \u00e9cho-endoscopie (septembre 2011) est r\u00e9alis\u00e9e montrant un pancr\u00e9as et des voies biliaires normales et de nombreux ad\u00e9nopathies de la r\u00e9gion inter-aortico-cave d\u2019allure inflammatoire de 4 cm de diam\u00e8tre. TDM thoraco-abdominale : ad\u00e9nopathies m\u00e9diastinales de 10-15 mm, m\u00e9sent\u00e9rique et r\u00e9tro-portes. La ponction biopsie sous \u00e9cho-endoscopie d\u2019une ad\u00e9nopathie montre de nombreux granulomes \u00e9pith\u00e9lio\u00efdes et giganto-cellulaires sans n\u00e9crose. Dosage du quantiferon normal, recherche de BK n\u00e9gative dans les crachats et les urines.<br \/>\nEOGD et il\u00e9o-coloscopie (f\u00e9vrier 2011) : normales. Pr\u00e9sence sur les biopsies fundiques et antrales d\u2019amas lympho\u00efdes avec quelques granulomes \u00e9pith\u00e9lio\u00efdes et giganto-cellulaires sans n\u00e9crose ; biopsies papillaires normales, dosage de l&#039; enzymz de conversion de l&#039; angiotensine \u00e0 140 UI\/l (N: 8-52 UI).<br \/>\nAucun traitement sp\u00e9cifique n\u2019est entrepris (notamment pas de cortico\u00efde).<br \/>\nLe 08\/05\/2012, date limite de soumission des abstracts, elle consulte \u00e0 nouveau pour apparition de volumineuses ad\u00e9nopathies cervicales avec r\u00e9cidive de la conjonctivite.<\/p>\n<p>Au total :<br \/>\nTableau inaugural de pancr\u00e9atite aigu\u00eb sans cause retrouv\u00e9e. Dans les 18 mois suivants ce premier \u00e9pisode, r\u00e9cidive de douleurs abdominales sans argument objectif de pancr\u00e9atite. Mise en \u00e9vidence d\u2019ad\u00e9nopathies diffuses, notamment de hilaire h\u00e9patique avec pr\u00e9sence de nombreux granulomes \u00e0 l\u2019histologie ganglionnaire et gastrique faisant \u00e9voquer une sarco\u00efdose. <\/p>\n<p>Commentaires :<br \/>\nLes localisations diogestives de la sarco\u00efdose sont rares (mais peut-\u00eatre sous-estim\u00e9es). L\u2019atteinte gastrique est de loin la plus fr\u00e9quente, mais peut \u00eatre asymptomatique, entra\u00eener des douleurs voire des h\u00e9morragies digestives avec \u00e0 l\u2019endoscopies des l\u00e9sions ulc\u00e9r\u00e9es, parfois un aspect de pseudo-linite.<br \/>\nL\u2019atteinte pancr\u00e9atique est tout \u00e0 fait exceptionnelle. Des cas de pancr\u00e9atite aigue \u00e9ventuellement r\u00e9cidivante, ont n\u00e9anmoins d\u00e9j\u00e0 \u00e9t\u00e9 rapport\u00e9s. Le principal diagnostic diff\u00e9rentiel est celui de pancr\u00e9atite auto-immune (\u00e9limin\u00e9 chez notre patiente par l\u2019aspect scannographique et \u00e9cho-endoscopique de la glande, l\u2019absence d\u2019\u00e9l\u00e9vation de l\u2019IgG 4 et des gammaglobulines). L\u2019atteinte pancr\u00e9atique peut se traduire par un aspect pseudo-tumoral unique ou multiple mais celui-ci est tr\u00e8s inconstamment retrouv\u00e9, notamment dans les cas rapport\u00e9s de pancr\u00e9atite aigue. Le m\u00e9canisme de la panc\u00e9atite n\u2019est pas clair, pouvant \u00eatre li\u00e9 \u00e0 une infiltration sarco\u00efdosique de la glande ou une hypercalc\u00e9mie dans le cadre de la sarco\u00efdose. Souvent, comme dans notre observation, aucun m\u00e9canisme ne peut \u00eatre mis en \u00e9vidence. Aucun cas de pancr\u00e9atite grave n\u2019a \u00e0 notre connaissance \u00e9t\u00e9 rapport\u00e9 dans la litt\u00e9rature, l\u2019\u00e9volution de la pancr\u00e9atite est le plus souvent b\u00e9nigne, parfois r\u00e9currente. Dans la plupart des cas, aucun traitement sp\u00e9cifique n\u2019a \u00e9t\u00e9 administr\u00e9, parfois cortico\u00efdes ou mycoph\u00e9nolate.<br \/>\nM\u00eame si l\u2019\u00e9tiologie sarco\u00efdosique est rare, elle doit \u00eatre \u00e9voqu\u00e9e devant une pancr\u00e9atite inexpliqu\u00e9e, notamment en cas d\u2019ad\u00e9nopathies profondes.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>2012 Laurence MARTIN. Jacques DENIS, Fatima DAOUDI, Leila MANSOUR, B\u00e9n\u00e9dicte LAMBARE Service h\u00e9pato gastro ent\u00e9rologie, Centre Hospitalier Sud Francilien, 116 Boulevard Jean Jaur\u00e8s, 91100 CORBEIL ESSONNES Gastroent\u00e9rologie &#8211; \u00a02012-05-04 &#8211;\u00a0Cho &#8211; ________________________________ Une patiente de 29 ans d\u2019origine maghr\u00e9bine sans ant\u00e9c\u00e9dent particulier, est hospitalis\u00e9e en urgence le 18\/02\/2011 pour violentes douleurs \u00e9pigastriques \u00e0 irradiation dorsale [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[4],"tags":[23],"class_list":["post-1941","post","type-post","status-publish","format-standard","hentry","category-gastroenterologie","tag-23"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.2 - 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