{"id":2023,"date":"2015-10-01T01:00:00","date_gmt":"2015-10-01T00:00:00","guid":{"rendered":"https:\/\/angh.net\/abstracts\/une-jaunisse-alcoolisee-sans-cirrhose-noubliez-pas-zieve\/"},"modified":"2018-10-20T18:40:15","modified_gmt":"2018-10-20T16:40:15","slug":"une-jaunisse-alcoolisee-sans-cirrhose-noubliez-pas-zieve","status":"publish","type":"post","link":"https:\/\/angh.net\/abstracts\/une-jaunisse-alcoolisee-sans-cirrhose-noubliez-pas-zieve\/","title":{"rendered":"Une jaunisse alcoolis\u00e9e sans cirrhose : n&rsquo;oubliez pas Zieve!"},"content":{"rendered":"<p><strong>2015<\/strong><\/p>\n<p><em>Matthieu Le Besco, Isabelle Rosa, Camille Barrault, Anne Laure Audrain, Emma Ferrand, Laurent Costes, Thierry Lons, Herv\u00e9 Hag\u00e8ge<\/em><\/p>\n<p><strong>H\u00e9patologie <\/strong>&#8211; \u00a02015-04-29 &#8211;\u00a0CC &#8211;<\/p>\n<p>________________________________<\/p>\n<p>Mr L., 32ans, se pr\u00e9sente pour ict\u00e8re \u00e9voluant depuis 10 jours, non prurigineux. Il pr\u00e9sente comme principal ant\u00e9c\u00e9dent un \u00e9thylisme chronique, avec une consommation de 100g d\u2019alcool par jour, qui s\u2019est major\u00e9e depuis 3 semaines. Il n\u2019a pas r\u00e9alis\u00e9 r\u00e9cemment de voyage.<br \/>\nA l\u2019entr\u00e9e son \u00e9tat h\u00e9modynamique est conserv\u00e9 . Il ne pr\u00e9sente pas de syndrome f\u00e9brile. L\u2019examen clinique n\u2019objective pas de signe d\u2019insuffisance  h\u00e9patocellaire, pas de signe d\u2019hypertension portale, pas de saignement externalis\u00e9.<br \/>\nLe bilan biologique r\u00e9alis\u00e9 objective une acidose m\u00e9tabolique (pH 7,32, HCO3-  10,5mmol\/l), une an\u00e9mie normocytaire r\u00e9g\u00e9n\u00e9rative (Hb 10g\/dl, VGM 98fl, r\u00e9ticulocytes 158 G\/l), un bilan h\u00e9patique perturb\u00e9 (ASAT 761 UI\/l, ALAT 134 UI\/l, PAL 412 UI\/l, GGT 5043 UI\/l, Bilirubine totale 300 \u00b5mol\/l, Bilirubine conjugu\u00e9e 173 \u00b5mol\/l, TP 21%, facteur II 42%, facteur V 117%), une hypokali\u00e9mie (K+ : 2,6 mmol\/l) sans insuffisance r\u00e9nale (cr\u00e9atinin\u00e9mie 77 \u00b5mol\/l, ur\u00e9e 1,8 mmol\/l), une hypoalbumin\u00e9mie (Alb 23 g\/l) et des lactates \u00e0 0,79 mmol\/l.<br \/>\nLe bilan d\u2019an\u00e9mie objective une an\u00e9mie h\u00e9molytique avec pr\u00e9sence de schizocytes sur le frottis sanguin, une diminution de l\u2019haptoglobine \u00e0 0,4g\/l, et une augmentation de la bilirubine libre et des LDH \u00e0 449 UI\/l.<br \/>\nAucune prise m\u00e9dicamenteuse n\u2019a \u00e9t\u00e9 rapport\u00e9e par le patient ou son entourage. La parac\u00e9tamol\u00e9mie \u00e9tait n\u00e9gative, Ainsi que la recherche de toxiques et de stup\u00e9fiants dans le sang et les urines. L\u2019alcool\u00e9mie \u00e0 l\u2019entr\u00e9e \u00e9tait de 0,55 g\/l. Les s\u00e9rologies virales A, B, C, E, VIH, CMV , EBV \u00e9taient n\u00e9gatives. Il n\u2019a pas \u00e9t\u00e9 mis en \u00e9vidence d\u2019infection bact\u00e9rienne sur les h\u00e9mocultures, et l\u2019examen cyto-bact\u00e9riologique des urines.  Le dosage pond\u00e9ral des immunoglobulines n\u2019objectivait pas d\u2019anomalie (IgA 2,10 g\/l, IgM 0,48 g\/l, IgG 4,74 g\/l), Les Ac anti-nucl\u00e9aires, anti-LKM, anti-cytosol, anti-mitochondrie, et anti-muscle lisse \u00e9taient n\u00e9gatifs. Le bilan du cuivre (c\u00e9ruloplasmine 2,39 \u00b5mol\/l, cupr\u00e9mie 1,18 mg\/l) \u00e9tait normal, contrairement au bilan du fer (fer s\u00e9rique 31 \u00b5mol\/l, ferritine 1964 \u00b5g\/l, coefficient de saturation de la transferrine 44%). Le bilan lipidique objectivait une hypercholest\u00e9rol\u00e9mie et une hypertriglyc\u00e9rid\u00e9mie (cholest\u00e9rol 7,6 mmol\/l, LDL 7,3 mmol\/l, triglyc\u00e9ride \u00e0 4,14 mmol\/l)<br \/>\nL\u2019\u00e9chographie-doppler h\u00e9patique montrait une h\u00e9patom\u00e9galie homog\u00e8ne, h\u00e9t\u00e9rog\u00e8ne, avec perm\u00e9abilit\u00e9 des axes vasculaires, et sans l\u00e9sion focale, sans dilation des voies biliaires.<br \/>\nLa ponction biopsie h\u00e9patique objectivait un parenchyme h\u00e9patique remani\u00e9, avec une fibrose reliant quelques septa. Cette fibrose \u00e9tant le si\u00e8ge d\u2019un infiltrat mononucl\u00e9e m\u00e9l\u00e9 \u00e0 de rares polynucl\u00e9aires. Importante st\u00e9atose micro et macrovacuolaire (95%). Pr\u00e9sence de rares foyers inflammatoires constitu\u00e9s d\u2019\u00e9l\u00e9ments lymphoplasmocytaires. Pr\u00e9sence \u00e9galement de pigments brun\u00e2tre correspondant \u00e0 la cholestase.  Il n\u2019existait pas d\u2019\u00e9l\u00e9ment en faveur d\u2019une h\u00e9patite alcoolique aigue.<br \/>\nUn traitement par Fluimicuil a \u00e9t\u00e9 instaur\u00e9 d\u00e8s le d\u00e9but de la prise en charge. Le sevrage a \u00e9t\u00e9 r\u00e9alis\u00e9 sous couvert d\u2019une hydratation associ\u00e9 \u00e0 une suppl\u00e9mentation vitaminique et des benzodiaz\u00e9pines de longue dur\u00e9e d\u2019action.<br \/>\nQuel est votre diagnostic ?<br \/>\nL\u2019association d\u2019un ict\u00e8re, avec une an\u00e9mie h\u00e9molytique et d\u2019une hyperlipid\u00e9mie chez un patient pr\u00e9sentant une alcoolisation aigue sur un terrain d\u2019alcoolisation chronique nous a fait poser le diagnostic de syndrome de Zieve.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>2015 Matthieu Le Besco, Isabelle Rosa, Camille Barrault, Anne Laure Audrain, Emma Ferrand, Laurent Costes, Thierry Lons, Herv\u00e9 Hag\u00e8ge H\u00e9patologie &#8211; \u00a02015-04-29 &#8211;\u00a0CC &#8211; ________________________________ Mr L., 32ans, se pr\u00e9sente pour ict\u00e8re \u00e9voluant depuis 10 jours, non prurigineux. Il pr\u00e9sente comme principal ant\u00e9c\u00e9dent un \u00e9thylisme chronique, avec une consommation de 100g d\u2019alcool par jour, qui [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[3],"tags":[26],"class_list":["post-2023","post","type-post","status-publish","format-standard","hentry","category-hepatologie","tag-26"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.2 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Une jaunisse alcoolis\u00e9e sans cirrhose : n&#039;oubliez pas Zieve! - Abstracts des congr\u00e8s de l&#039;ANGH<\/title>\n<meta name=\"description\" content=\"ANGH R\u00e9sum\u00e9s congr\u00e8s H\u00e9patologie Gastroent\u00e9romogie Hepatology Gastroenterology Etudes cliniques Clinical study\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/angh.net\/abstracts\/une-jaunisse-alcoolisee-sans-cirrhose-noubliez-pas-zieve\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Une jaunisse alcoolis\u00e9e sans cirrhose : n&#039;oubliez pas Zieve! 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