{"id":2383,"date":"2021-10-06T13:54:23","date_gmt":"2021-10-06T11:54:23","guid":{"rendered":"https:\/\/angh.net\/abstracts\/une-diarrhee-chronique-chez-une-patiente-atypique\/"},"modified":"2021-10-06T14:15:26","modified_gmt":"2021-10-06T12:15:26","slug":"une-diarrhee-chronique-chez-une-patiente-atypique","status":"publish","type":"post","link":"https:\/\/angh.net\/abstracts\/une-diarrhee-chronique-chez-une-patiente-atypique\/","title":{"rendered":"Une diarrh\u00e9e chronique chez une patiente atypique"},"content":{"rendered":"<p><strong>2021<\/strong><\/p>\n<p><em>Dany Rizk1, Julia Roux1, Anne-Laure Desgabriel1, Sihem Asselah1, Danielle Jaafar2, Armand Garioud1.<br \/>\n1. Service d\u2019h\u00e9pato-gastroent\u00e9rologie \u2013 CHI de Villeneuve-Saint-Georges.<br \/>\n2. Service de m\u00e9decine infectieuse et tropicale \u2013 CHI de Villeneuve-Saint-Georges.<\/em><\/p>\n<p><strong>Gastroent\u00e9rologie\u00a0<\/strong>&#8211; \u00a02021-05-22 &#8211;\u00a0CC &#8211;<\/p>\n<p>________________________________<\/p>\n<p>Une patiente de 29 ans sans ant\u00e9c\u00e9dent particulier et sans notion de voyage \u00e0 l\u2019\u00e9tranger a \u00e9t\u00e9 hospitalis\u00e9e par les Urgences en ao\u00fbt 2020 pour l\u2019exploration d\u2019une alt\u00e9ration de l&rsquo;\u00e9tat g\u00e9n\u00e9ral avec paresth\u00e9sies et faiblesse musculaire des 4 membres associ\u00e9es \u00e0 une anorexie et une perte de poids depuis 2 mois. On notait une diarrh\u00e9e chronique non glairo-sanglante pr\u00e9sente depuis 2 ans avec 4-5 selles par jour -dont des selles nocturnes- qui s\u2019est aggrav\u00e9e depuis 3 semaines. Elle ne prenait pas de traitement particulier.<\/p>\n<p>Cliniquement, la patiente n\u2019a jamais \u00e9t\u00e9 f\u00e9brile. Elle pesait 102kgs (BMI 39). Il existait un d\u00e9ficit sensitivomoteur des 4 membres plus prononc\u00e9 au niveau inf\u00e9rieur avec une incontinence f\u00e9cale et urinaire occasionnelle. Les ROTs \u00e9taient faibles sans signe de Babinski. Elle marchait en d\u00e9ambulateur. L\u2019\u00e9valuation psychiatrique a r\u00e9v\u00e9l\u00e9 un trouble de la personnalit\u00e9 type \u00ab borderline \u00bb. L\u2019examen cutan\u00e9 a permis de relever la pr\u00e9sence de placards pigment\u00e9s des membres inf\u00e9rieurs et de la face externe des bras, des l\u00e9sions v\u00e9siculeuses et ulc\u00e9r\u00e9es du sillon interfessier ainsi que des ulc\u00e8res de la langue et de la cavit\u00e9 buccale. La palpation abdominale \u00e9tait sans particularit\u00e9.<\/p>\n<p>La biologie objectivait une an\u00e9mie \u00e0 5,4 g\/dl, macrocytaire (VGM 114), ar\u00e9g\u00e9n\u00e9rative (r\u00e9ticulocytes 7,4 G\/L) avec des stigmates d&rsquo;h\u00e9molyse (haptoglobine effondr\u00e9e, LDH augment\u00e9s \u00e0 1819 U\/l). La recherche de schizocytes et le test de Coombs \u00e9rythrocytaire \u00e9taient n\u00e9gatifs. Il existait un syndrome inflammatoire : GB 11,7 G\/L, CRP 70 mg\/l, ferritin\u00e9mie 528 ng\/ml. La fonction r\u00e9nale \u00e9tait normale. Les tests h\u00e9patiques \u00e9taient subnormaux (AST 1,5N, ALT N, GGT N, PAL 1,3N, BiliT 25\u00b5mol\/l, BiliC 8\u00b5mol\/l) et il existait des stigmates de d\u00e9nutrition (albumin\u00e9mie 19g\/l, carences vitaminiques multiples en vit A, B1, B6, C, D et s\u00e9l\u00e9nium. Les folates \u00e9taient effondr\u00e9s et la vit B12 \u00e9taint normale de m\u00eame que la TSH. Il n\u2019y avait pas d\u2019argument pour une maladie coeliaque (IgA s\u00e9riques normaux, Ac anti-transglutaminases et anti-gliadine n\u00e9gatifs).<\/p>\n<p>Le bilan infectieux n\u2019a pas mis en \u00e9vidence de point d\u2019appel : PCR SARS-CoV-2 n\u00e9gative, h\u00e9mocultures n\u00e9gatives, ECBU n\u00e9gatif, coproculture + toxine Clostridium difficile n\u00e9gative. La s\u00e9rologie VHB \u00e9tait de profil post-vaccinal et les s\u00e9rologies VIH et VHC \u00e9taient n\u00e9gatives. La PCR CMV sang \u00e9tait n\u00e9gative de m\u00eame que les PCR HSV1 et 2 tant sur un \u00e9couvillon buccal et des v\u00e9sicules fessi\u00e8res qu\u2019au niveau du sang. La recherche de frottis &#8211; goutte \u00e9paisse \u00e9tait n\u00e9gative.<\/p>\n<p>La patiente a \u00e9t\u00e9 transfus\u00e9e de 5 culots globulaires avec un bon rendement et une renutrition avec de multiples suppl\u00e9mentations a \u00e9t\u00e9 d\u00e9but\u00e9e. Le bilan endoscopique digestif a objectiv\u00e9 une oesophagite ulc\u00e9r\u00e9e des 1\/3 moyen et inf\u00e9rieur, une gastrite\/bulbite sans signe de sp\u00e9cificit\u00e9. Sur les biopsies, il existait une duod\u00e9nite chronique non sp\u00e9cifique, une gastrite chronique discr\u00e8te sans Helicobacter pylori et une \u0153sophagite sans mise en \u00e9vidence de filaments myc\u00e9liens ou d\u2019\u00e9l\u00e9ment viral (PCR HSV1 et HSV2 n\u00e9gatives). L\u2019il\u00e9ocoloscopie totale Boston 9 a objectiv\u00e9 une il\u00e9ite \u00e9ryth\u00e9mateuse sur les tout derniers cm avec une valvule il\u00e9o caecale ulc\u00e9r\u00e9e. Sur les biopsies, il existait une discr\u00e8te hyperplasie lympho\u00efde de la muqueuse il\u00e9ale sans \u00e9l\u00e9ment suspect. La muqueuse colique \u00e9tait peu modifi\u00e9e hormis au niveau de la valvule o\u00f9 il existait des l\u00e9sions de colite aigu\u00eb non sp\u00e9cifique sans argument pour une maladie de Crohn (absence de granulome). Les pr\u00e9l\u00e8vements histologiques pour recherche de BK et PCR CMV \u00e9taient n\u00e9gatifs. L\u2019ent\u00e9ro-IRM qui a \u00e9t\u00e9 faite a permis d\u2019objectiver un discret \u00e9paississement pari\u00e9tal de la derni\u00e8re anse il\u00e9ale sur 4 cm de longueur mais sans signe franc d&rsquo;il\u00e9ite terminale et sans collection ou trajet fistuleux identifiable.<\/p>\n<p>Des explorations neurologiques ont \u00e9galement \u00e9t\u00e9 effectu\u00e9es avec un EMG qui a confirm\u00e9 la pr\u00e9sence d\u2019une polyneuropathie s\u00e9v\u00e8re axonale sensitivomotrice \u00e0 pr\u00e9dominance sensitive. Quant \u00e0 l\u2019IRM m\u00e9dullaire, elle \u00e9tait normale. L\u2019ensemble \u00e9voquait une atteinte neurologique d\u2019origine carentielle. L\u2019ETT \u00e9tait normale sans argument pour une cardiopathie carentielle.<\/p>\n<p>Quel est votre hypoth\u00e8se diagnostique concernant cette diarrh\u00e9e chronique ?<br \/>\nQuel examen fait pendant les endoscopies digestives attendez-vous pour le confirmer ?<br \/>\nCelui-ci reviendra positif\u2026 La suite du cas clinique vous sera pr\u00e9sent\u00e9e lors du congr\u00e8s avec une revue bibliographique.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>2021 Dany Rizk1, Julia Roux1, Anne-Laure Desgabriel1, Sihem Asselah1, Danielle Jaafar2, Armand Garioud1. 1. Service d\u2019h\u00e9pato-gastroent\u00e9rologie \u2013 CHI de Villeneuve-Saint-Georges. 2. Service de m\u00e9decine infectieuse et tropicale \u2013 CHI de Villeneuve-Saint-Georges. Gastroent\u00e9rologie\u00a0&#8211; \u00a02021-05-22 &#8211;\u00a0CC &#8211; ________________________________ Une patiente de 29 ans sans ant\u00e9c\u00e9dent particulier et sans notion de voyage \u00e0 l\u2019\u00e9tranger a \u00e9t\u00e9 hospitalis\u00e9e par [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[4],"tags":[34],"class_list":["post-2383","post","type-post","status-publish","format-standard","hentry","category-gastroenterologie","tag-34"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.2 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Une diarrh\u00e9e chronique chez une patiente atypique - Abstracts des congr\u00e8s de l&#039;ANGH<\/title>\n<meta name=\"description\" content=\"ANGH R\u00e9sum\u00e9s congr\u00e8s H\u00e9patologie Gastroent\u00e9romogie Hepatology Gastroenterology Etudes cliniques Clinical study\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/angh.net\/abstracts\/une-diarrhee-chronique-chez-une-patiente-atypique\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Une diarrh\u00e9e chronique chez une patiente atypique - 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